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Journal Information
Vol. 65. Issue 4.
Pages 347-348 (April 1999)
Vol. 65. Issue 4.
Pages 347-348 (April 1999)
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Útero didelfo, hemihematometrocolpos y agenesia del árbol urinario homolateral. Presentación de dos casos
UTERINE DIDELPHYS, HEMI-HEMATOMETROCOLPOS AND HOMOLATERAL AGENESIS OF THE URINARY TRACT. REPORT OF TWO CASES
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LE. Marcano Sanz, G. Siax Carmenate, G. Nodarse Fernández, Y. Hidalgo Marrero
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Article information
Presentamos una rara anomalía del aparato genitourinario en la cual se asocian útero didelfo, vagina ciega y agenesia del árbol urinario homolateral en 2 adolescentes con antecedentes de dismenorrea en las cuales, como en la mayoría de los casos, la presentación clínica fue el dolor abdominal paroxístico. Comentamos la embriología de esta enfermedad y las teorías descritas para intentar explicar su etiología, así como los procederes diagnósticos y terapéuticos requeridos en estos casos.
Palabras clave:
Hematometrocolpo
Dismenorrea
Agenesia renal
We present a rare malformation of the genitourinary tract comprised of the association of uterine didelphys, imperforate vagina and homolateral agenesis of the urinary tract in two adolescents with a history of dysmenorrhea. In both, as in most cases, the presenting sign was paroxysmal abdominal pain. We discuss the embryological factors associated with this defect and the existing theories concerning the etiology. The diagnostic and therapeutic procedures involved in these cases are also described.
Keywords:
Hematometrocolpos
Dysmenorrhea
Renal agenesis