Article information
Abstract
Congenital dilations of the biliary tract are a group of rare conditions, commonly associated with the presence of an abnormality at the junction of the common bile duct and pancreatic duct, which may lead to the reflux of pancreatic juice within the biliary tree. The main clinical symptoms are, abdominal pain, cholangitis and acute pancreatitis, and the most serious complication is malignant degeneration. The treatment of choice is cholecystectomy and complete excision of the bile duct from its bifurcation to its intra-pancreatic segment.
Keywords:
Congenital dilation of bile duct
Choledochal cyst
Abnormality of the biliopancreatic junction
Resumen
Las dilataciones congénitas de la vía biliar son un grupo de alteraciones poco frecuentes, comúnmente asociadas con la presencia de una anomalía de la unión del conducto biliar con el conducto pancreático que favorece el reflujo de jugo pancreático en el interior del árbol biliar. Las principales manifestaciones clínicas son el dolor abdominal, la colangitis y la pancreatitis aguda, y la complicación más grave es la degeneración maligna. El tratamiento de elección es la colecistectomía y la exéresis completa de la vía biliar, desde su bifurcación hasta su porción intrapancreática.
Palabras clave:
Dilatación congénita de la vía biliar
Quiste de colédoco
Anomalía de la unión biliopancreática
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