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Vol. 99. Issue 2.
Pages 33-37 (January 2002)
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Vol. 99. Issue 2.
Pages 33-37 (January 2002)
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Conceptos generales sobre el metabolismo del hierro
General basis of iron metabolism
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J.J. Alonso, A. Cánovas, R. De la Prieta, T. Pereira, C. Ruiz, C. Aguirre
Servicio de Medicina Interna y Cátedra de Medicina Interna. UPV/EHU. Hospital de Cruces. Barakaldo.
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Resumen

La regulación del metabolismo del hierro, tanto en lo referido a la limitación de su absorción intestinal como a su distribución en diferentes células y compartimentos intracelulares, sigue escapando a nuestra comprensión, pero los estudios sobre este tema han aportado nuevas luces e incógnitas. Se han ido conociendo proteínas que participan en diferentes etapas del metabolismo férrico: integrinas, movilferrina y DMT-1 en la absorción intestinal; ferroportina y hefestina en la transmisión del hierro desde el enterocito a la transferrina circulante; receptor de transferrina para la captación celular de hierro; proteínas reguladoras del hierro (IRP) y elementos sensibles a hierro (IRE) para controlar la concentración intracelular de hierro metabólicamente activo. Los nuevos hallazgos tienen por el momento una repercusión limitada en la actividad clínica rutinaria, pero no pueden ser ignorados al afrontar todo lo relacionado con este tema.

Summary

Iron metabolism regulation as for the limitation of intestinal absortion and distribution to different cells and cellular compartments remains a mistery to us. However recent researchs on this issue provide both clarifying facts and new riddles to solve. New proteins taking part in different stages of iron metabolism have come into play: integrin, mobilferrin and DMT-1 in intestinal absortion; ferroportin and haephestin related to iron release to transferrin from the enterocyte; transferrin receptor for iron uptake by cells, and iron regulatory proteins (IRP) and iron responsive elements (IRE) in management of intracellular level of active iron. Despite its momentary limited repercusion in ordinary clinical labour these findings can never be ignored as far as iron related pathology is concerned

Laburpena

Burdinaren metabolismoaren erregulazioak, bai heste-xurgapenaren mugapenari dagokionez, bai zeluletan eta zelula-barneko konpartimentuetan banatzeari dagokionez, ezezagun samarra izaten jarraitzen badu ere, harekin lotutako hainbat aurkikuntza egin dira azkenaldian. Hala, burdinaren metabolismoaren etapetan parte hartzen duten proteina batzuk aurkitu dira: integrina, mobilferrina eta DMT-1, heste-xurgapenean; ferroportina eta hefestina, enterozitoaren eta zirkulazioan dagoen transferrinaren arteko burdina transmisioan; transferrina hartzailea, burdinaren atzitze zelularrerako; burdinaren proteina erregulatzaileak (IRP) eta burdinarekiko elementu sentikorrak (IRE), metabolikoki aktiboa den burdinaren zelula-barneko kontzentrazioa kontrolatzeko. Aurkikuntzez oraingoz eguneroko jarduera klinikoan eragin handiegirik izango ez badute ere, ezin dira bazter batean utzi eta kontuan hartzea merezi dute.

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Copyright © 2002. Academia de Ciencias Médicas de Bilbao
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