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RESUMEN
Presentamos el caso de un niño con síndrome de Freeman-Sheldon programado para la corrección quirúrgica de su microstomia. El niño presentaba la característica de “cara de silvador” y deformidades de artrogriposis en manos y pies. Se expone el manejo anestésico y de la vía aérea
Palabras clave:
Síndrome de Freeman-Sheldon (SFS)
Síndrome de “cara en silbido”
Vía aérea difícil en pediatría
Artrogriposis
SUMMARY
We describe a case of a child with typical clinical features of Freeman-Sheldon syndrome (FSS) presented for elective surgical correction of microstomia. The anaesthetic and airway problems encountered are discussed.
Key words:
Freeman-Sheldon syndrome
Whistling face syndrome
Arthrogryposis, Airway management
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