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Inicio Revista Española de Patología Distrofia de membrana basal epitelial corneal: a propósito de un caso
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Vol. 56. Issue 2.
Pages 136-139 (April - June 2023)
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Vol. 56. Issue 2.
Pages 136-139 (April - June 2023)
ARTÍCULO BREVE
Distrofia de membrana basal epitelial corneal: a propósito de un caso
Epithelial basement membrane corneal dystrophy: A case report
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Carolina Díaz Baena
Corresponding author
cdiazbaena@hotmail.es

Autor para correspondencia.
, Elena Gallego Domínguez, María Isabel Hierro Martín
Departamento de Anatomía Patológica, Hospital Universitario Virgen de la Victoria, Málaga, España
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Rev Esp Patol. 2023;56:e1-e510.1016/j.patol.2023.04.001
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Resumen

La distrofia de la membrana basal epitelial corneal es una entidad poco frecuente, que se presenta en forma de erosiones corneales de repetición debidas a una alteración en la unión del epitelio corneal a la membrana basal. Esta patología ha sido presentada en la literatura con un enfoque eminentemente oftalmológico, dejando en un segundo plano la anatomía patológica. El objetivo de este artículo es resaltar la imagen microscópica de esta patología a propósito de un caso, así como realizar una aproximación clínica y terapéutica de esta entidad.

Palabras clave:
Distrofia de la membrana basal epitelial corneal
Distrofia en mapa-punto-huella
Erosiones corneales de repetición
Anatomía patológica
Abstract

Epithelial basement membrane corneal dystrophy is a rare entity, characterized by recurrent corneal erosions secondary to a disorder in the attachment of the corneal epithelium to the basement membrane. To date, mainly the ophthalmological aspect of cases has been reported, with little emphasis on the pathology of this lesion. Here we aim to describe the microscopy and discuss the clinical and therapeutic aspects of a case.

Keywords:
Epithelial basal membrane dystrophy
Map-dot-fingerprint dystrophy
Recurrent corneal erosions
Pathology

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