Recurrent Meningitis Associated With Duane Syndrome Type 1

Abstract

We present the case of a 17-month-old male patient with a bilateral Duane syndrome type 1 associated to unilateral cochleovestibular dysplasia, perilymphatic fistula and recurrent meningitis. Diagnosis was carried out by MRI and CT scan. His management and treatment are described, as well as the postoperative evolution. We believe this is an exceptional case due to the low frequency of this syndrome, as well as to the otoneurological complications.

Resumen

Presentamos el caso de un paciente varón de 17 meses con síndrome de Duane tipo 1 bilateral asociado a displasia cocleovestibular unilateral, fístula perilinfática y meningitis de repetición. El diagnóstico se realizó mediante TC de peñascos y RM cerebral. Se describe su manejo y tratamiento, así como la evolución postoperatoria. Debido a la poca frecuencia de este síndrome, así como a la de sus complicaciones de tipo otoneurológico, consideramos que se trata de un caso excepcional.