array:23 [ "pii" => "S003383380176955X" "issn" => "00338338" "doi" => "10.1016/S0033-8338(01)76955-X" "estado" => "S300" "fechaPublicacion" => "2001-01-01" "aid" => "76955" "copyright" => "Sociedad Española de Radiología Médica (SERAM) and Elsevier España, S.L." "copyrightAnyo" => "2001" "documento" => "article" "crossmark" => 0 "subdocumento" => "fla" "cita" => "Radiologia. 2001;43:197-201" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:2 [ "total" => 7348 "formatos" => array:3 [ "EPUB" => 10 "HTML" => 5984 "PDF" => 1354 ] ] "itemSiguiente" => array:18 [ "pii" => "S0033833801769561" "issn" => "00338338" "doi" => "10.1016/S0033-8338(01)76956-1" "estado" => "S300" "fechaPublicacion" => "2001-01-01" "aid" => "76956" "copyright" => "Sociedad Española de Radiología Médica (SERAM) and Elsevier España, S.L." "documento" => "article" "crossmark" => 0 "subdocumento" => "fla" "cita" => "Radiologia. 2001;43:202-5" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:2 [ "total" => 3962 "formatos" => array:3 [ "EPUB" => 9 "HTML" => 3363 "PDF" => 590 ] ] "es" => array:10 [ "idiomaDefecto" => true "titulo" => "Tumor desmoplásico de células redondas pequeñas: presentación de dos casos y revisión de la bibliografía<a class="elsevierStyleCrossRef" href="#fn0005">*</a>" "tienePdf" => "es" "tieneTextoCompleto" => 0 "tieneResumen" => array:2 [ 0 => "es" 1 => "en" ] "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "202" "paginaFinal" => "205" ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "Desmoplastic small round cell tumor: a report of two cases and a review of the literature" ] ] "contieneResumen" => array:2 [ "es" => true "en" => true ] "contienePdf" => array:1 [ "es" => true ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "Eduardo Ruiz, Genaro López, Carlos Touma, Angel Concha" "autores" => array:4 [ 0 => array:2 [ "nombre" => "Eduardo" "apellidos" => "Ruiz" ] 1 => array:2 [ "nombre" => "Genaro" "apellidos" => "López" ] 2 => array:2 [ "nombre" => "Carlos" "apellidos" => "Touma" ] 3 => array:2 [ "nombre" => "Angel" "apellidos" => "Concha" ] ] ] ] ] "idiomaDefecto" => "es" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0033833801769561?idApp=UINPBA00004N" "url" => "/00338338/0000004300000004/v1_201307311029/S0033833801769561/v1_201307311029/es/main.assets" ] "itemAnterior" => array:18 [ "pii" => "S0033833801769548" "issn" => "00338338" "doi" => "10.1016/S0033-8338(01)76954-8" "estado" => "S300" "fechaPublicacion" => "2001-01-01" "aid" => "76954" "copyright" => "Sociedad Española de Radiología Médica (SERAM) and Elsevier España, S.L." "documento" => "article" "crossmark" => 0 "subdocumento" => "fla" "cita" => "Radiologia. 2001;43:194-6" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:2 [ "total" => 3066 "formatos" => array:3 [ "EPUB" => 8 "HTML" => 2408 "PDF" => 650 ] ] "es" => array:10 [ "idiomaDefecto" => true "titulo" => "Rotura espontánea de un seudoquiste mesentérico no pancreático<a class="elsevierStyleCrossRef" href="#fn0005">*</a>" "tienePdf" => "es" "tieneTextoCompleto" => 0 "tieneResumen" => array:2 [ 0 => "es" 1 => "en" ] "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "194" "paginaFinal" => "196" ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "Spontaneous rupture of a nonpancreatic mesenteric pseudocyst" ] ] "contieneResumen" => array:2 [ "es" => true "en" => true ] "contienePdf" => array:1 [ "es" => true ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "José Francisco Ramón, Carlos Ortí, Encarnación Andrada" "autores" => array:3 [ 0 => array:2 [ "nombre" => "José Francisco" "apellidos" => "Ramón" ] 1 => array:2 [ "nombre" => "Carlos" "apellidos" => "Ortí" ] 2 => array:2 [ "nombre" => "Encarnación" "apellidos" => "Andrada" ] ] ] ] ] "idiomaDefecto" => "es" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0033833801769548?idApp=UINPBA00004N" "url" => "/00338338/0000004300000004/v1_201307311029/S0033833801769548/v1_201307311029/es/main.assets" ] "es" => array:15 [ "idiomaDefecto" => true "titulo" => "Síndrome de Noonan y quilotórax<a class="elsevierStyleCrossRef" href="#fn0005">*</a>" "tieneTextoCompleto" => 0 "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "197" "paginaFinal" => "201" ] ] "autores" => array:1 [ 0 => array:4 [ "autoresLista" => "María I. Martínez-León, Luisa Ceres-Ruiz, Ramón Solbes-Vila, Esperanza Valls-Moreno" "autores" => array:4 [ 0 => array:4 [ "nombre" => "María I." "apellidos" => "Martínez-León" "email" => array:1 [ 0 => "marcela337@hotmail.com" ] "referencia" => array:1 [ 0 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">†</span>" "identificador" => "cor0005" ] ] ] 1 => array:2 [ "nombre" => "Luisa" "apellidos" => "Ceres-Ruiz" ] 2 => array:2 [ "nombre" => "Ramón" "apellidos" => "Solbes-Vila" ] 3 => array:2 [ "nombre" => "Esperanza" "apellidos" => "Valls-Moreno" ] ] "afiliaciones" => array:1 [ 0 => array:1 [ "entidad" => "<span class="elsevierStyleItalic">Servicio de Radiodiagnóstico. Radiología Pediátrica. Hospital Materno-Infantil del C.H.U. «Carlos Haya». Málaga.</span>" ] ] "correspondencia" => array:1 [ 0 => array:3 [ "identificador" => "cor0005" "etiqueta" => "†" "correspondencia" => "MARÍA I. MARTÍNEZ-LEÓN. Av. Pintor Sorolla, 16, 1.<span class="elsevierStyleSup">o</span>29016 Málaga." ] ] ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "Noonan syndrome and chylothorax" ] ] "pdfFichero" => "main.pdf" "tienePdf" => true "fechaRecibido" => "2000-12-01" "fechaAceptado" => "2001-04-20" "PalabrasClave" => array:2 [ "es" => array:1 [ 0 => array:4 [ "clase" => "keyword" "titulo" => "Palabras clave" "identificador" => "xpalclavsec227012" "palabras" => array:3 [ 0 => "Síndrome de Noonan" 1 => "Quilotórax. Linfangiectasia" 2 => "Pediatría" ] ] ] "en" => array:1 [ 0 => array:4 [ "clase" => "keyword" "titulo" => "Key words" "identificador" => "xpalclavsec227011" "palabras" => array:4 [ 0 => "Noonan syndrome" 1 => "Chylothorax" 2 => "Lymphangiectasis" 3 => "Pediatrics" ] ] ] ] "tieneResumen" => true "resumen" => array:2 [ "es" => array:2 [ "titulo" => "Resumen" "resumen" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">El quilotórax en la edad pediátrica generalmente se desarrolla en complicaciones posquirúrgicas de cirugía cardiotorácica y raramente se debe a malformaciones del sistema linfático asociado a síndromes dismórficos. Presentamos dos casos de Síndrome de Noonan con desa-rrollo de quilotórax neonatal. Ante pacientes con fenotipo Noonan y derrame pleural que se desarrolle en el período neonatal, sin antece-dente de trauma obstétrico, está indicado descartar malformación linfá-tica congénita y estudiar el derrame pleural para realizar tratamiento inicial conservador con dieta. Radiografía de tórax, ecografía y TC to-rácico muestran el derrame pleural y patrón parenquimatoso compatibles con quilotórax y linfangiectasias.</p>" ] "en" => array:2 [ "titulo" => "Abstract" "resumen" => "<p id="spar0010" class="elsevierStyleSimplePara elsevierViewall">Chylothorax during childhood usually develops as a result of postoperative complications following cardiothoracic surgery. It is rarely due to the malformations of the lymphatic system associated with dys-morphic syndrome. We report two cases of Noonan syndrome involving neonatal development of chylothorax. In children with the Noonan phenotype who develop pleural effusion during the neonatal period in the absence of obstetric trauma, it is advisable to rule out the presence of congenital lymphatic malformation and study the pleural effusion, initially introducing conservative treatment with dietary therapy. Chest radiography, ultrasound and computed tomography reveal the presence of the pleural effusion and parenchymal pattern compatible with chylothorax and lymphangiectasis.</p>" ] ] "NotaPie" => array:1 [ 0 => array:2 [ "etiqueta" => "*" "nota" => "<p class="elsevierStyleNotepara">Martínez-León MI, Ceres-Ruiz L, Solbes-Vila R, et al. Síndrome de Noonan y quilotórax. Radiología 2001;43(4):197-201.</p>" ] ] "bibliografia" => array:2 [ "titulo" => "Bibliografía" "seccion" => array:1 [ 0 => array:2 [ "identificador" => "bibs0005" "bibliografiaReferencia" => array:15 [ 0 => array:3 [ "identificador" => "bib0005" "etiqueta" => "1." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Lymphatic dysplasia in a neonate with Noonan’s syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "F.H. Bloonfield" 1 => "W. Hadden" 2 => "T.R. Gunn" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1007/s002470050139" "Revista" => array:6 [ "tituloSerie" => "Pediatr Radiol" "fecha" => "1997" "volumen" => "27" "paginaInicial" => "321" "paginaFinal" => "323" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9094239" "web" => "Medline" ] ] ] ] ] ] ] ] 1 => array:3 [ "identificador" => "bib0010" "etiqueta" => "2." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Síndrome de Noonan y Avances" "autores" => array:1 [ 0 => array:2 [ "colaboracion" => "Grupo Andaluz de Endocrinología Pediátrica" "etal" => false ] ] ] ] "host" => array:1 [ 0 => array:1 [ "LibroEditado" => array:1 [ "serieFecha" => "1998" ] ] ] ] ] ] 2 => array:3 [ "identificador" => "bib0015" "etiqueta" => "3." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Syndrome of the month: Noonan syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:1 [ 0 => "J.E. Allanson" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "J Med Genet" "fecha" => "1987" "volumen" => "24" "paginaInicial" => "9" "paginaFinal" => "13" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/3543368" "web" => "Medline" ] ] ] ] ] ] ] ] 3 => array:3 [ "identificador" => "bib0020" "etiqueta" => "4." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Noonan syndrome presented with cystic hygroma and chylothorax: a case report" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "H.C. Huang" 1 => "T.J. Wang" 2 => "C.B. Huang" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Chang Keng i Hsueh Tsa Chih [resumen]" "fecha" => "1999" "volumen" => "22" "numero" => "2" "paginaInicial" => "313" "paginaFinal" => "318" ] ] ] ] ] ] 4 => array:3 [ "identificador" => "bib0025" "etiqueta" => "5." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Management of postoperative chylothorax with nitric oxide: a case report" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "J.W. Berkenbosch" 1 => "D.E. Withington" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Crit Care Med" "fecha" => "1999" "volumen" => "27" "paginaInicial" => "1022" "paginaFinal" => "1024" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/10362431" "web" => "Medline" ] ] ] ] ] ] ] ] 5 => array:3 [ "identificador" => "bib0030" "etiqueta" => "6." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Noonan syndrome with spontaneous chylothorax at birth [resumen]" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "D.K. Chan" 1 => "N.K. Ho" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Aus Paediatr J" "fecha" => "1989" "volumen" => "25" "numero" => "5" "paginaInicial" => "296" "paginaFinal" => "298" ] ] ] ] ] ] 6 => array:3 [ "identificador" => "bib0035" "etiqueta" => "7." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Spontaneous chylothorax in Noonan syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "M.B. Goens" 1 => "D. Campbell" 2 => "J. Wiggins" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "AJDC" "fecha" => "1992" "volumen" => "146" "paginaInicial" => "1453" "paginaFinal" => "1456" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/1456257" "web" => "Medline" ] ] ] ] ] ] ] ] 7 => array:3 [ "identificador" => "bib0040" "etiqueta" => "8." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Chylothorax in children: guidelines for diagnosis and management" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "V. Bütikker" 1 => "S. Fanconi" 2 => "R. Burguer" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:7 [ "tituloSerie" => "Chest" "fecha" => "1999" "volumen" => "116" "numero" => "3" "paginaInicial" => "682" "paginaFinal" => "687" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/10492271" "web" => "Medline" ] ] ] ] ] ] ] ] 8 => array:3 [ "identificador" => "bib0045" "etiqueta" => "9." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Postoperative chylothorax in children: differences between vascular and traumatic origin" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:1 [ 0 => "Coultre C Le" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:7 [ "tituloSerie" => "J Pediatr Surg" "fecha" => "1991" "volumen" => "26" "numero" => "5" "paginaInicial" => "519" "paginaFinal" => "523" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/2061800" "web" => "Medline" ] ] ] ] ] ] ] ] 9 => array:3 [ "identificador" => "bib0050" "etiqueta" => "10." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Anatomic variation of the thoracic duct and visualization of mediastinal lymph nodes, a lymphographic study" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "E.M. Cha" 1 => "P. Sirijintakam" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1148/119.1.45" "Revista" => array:6 [ "tituloSerie" => "Radiology" "fecha" => "1976" "volumen" => "119" "paginaInicial" => "45" "paginaFinal" => "48" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/1257453" "web" => "Medline" ] ] ] ] ] ] ] ] 10 => array:3 [ "identificador" => "bib0055" "etiqueta" => "11." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Pulmonary lymphangiestasis in Noonan syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "R.J. Hernández" 1 => "A.M. Stern" 2 => "A. Rosenthal" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.2214/ajr.134.1.75" "Revista" => array:6 [ "tituloSerie" => "AJR" "fecha" => "1980" "volumen" => "134" "paginaInicial" => "75" "paginaFinal" => "80" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/6766041" "web" => "Medline" ] ] ] ] ] ] ] ] 11 => array:3 [ "identificador" => "bib0060" "etiqueta" => "12." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Linfangiectasia pulmonar congénita y otras malformaciones asocia-das: a propósito de dos observaciones" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:6 [ 0 => "P. Moros" 1 => "I. Molina" 2 => "J.A. Ruiz" 3 => "P. Gimeno" 4 => "A. Marco" 5 => "C. Yus" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "An Esp Pediatr" "fecha" => "1999" "volumen" => "51" "paginaInicial" => "540" "paginaFinal" => "542" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/10652808" "web" => "Medline" ] ] ] ] ] ] ] ] 12 => array:3 [ "identificador" => "bib0065" "etiqueta" => "13." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Forme inhabituelle du syndrome de Noonan: expression néonatale pluriviscérale avec chylothorax et cutis verticis gyrata naevoïde" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:7 [ 0 => "P. Masson" 1 => "M. Fayon" 2 => "T. Lamireau" 3 => "B. Llanas" 4 => "D. Lacombe" 5 => "A. Taïeb" 6 => "J.L. Demarquez" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Pédiatrie" "fecha" => "1993" "volumen" => "48" "paginaInicial" => "59" "paginaFinal" => "62" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/8392694" "web" => "Medline" ] ] ] ] ] ] ] ] 13 => array:3 [ "identificador" => "bib0070" "etiqueta" => "14." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Noonan’s syndrome associated with neuroblastoma: a case report" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:3 [ 0 => "Miranda B López" 1 => "S.J. Westra" 2 => "S. Yazdani" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1007/s002470050140" "Revista" => array:6 [ "tituloSerie" => "Pediatr Radiol" "fecha" => "1997" "volumen" => "27" "paginaInicial" => "324" "paginaFinal" => "326" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9162899" "web" => "Medline" ] ] ] ] ] ] ] ] 14 => array:3 [ "identificador" => "bib0075" "etiqueta" => "15." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "3D MR lymphangiography: a new MR imaging method for the lymph vessels without contrast agent" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "S. Hayashi" 1 => "M. Miyazaki" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "Toshiba Medical Review" "fecha" => "2000" "volumen" => "72" "paginaInicial" => "42" "paginaFinal" => "45" ] ] ] ] ] ] ] ] ] ] ] "idiomaDefecto" => "es" "url" => "/00338338/0000004300000004/v1_201307311029/S003383380176955X/v1_201307311029/es/main.assets" "Apartado" => array:4 [ "identificador" => "8111" "tipo" => "SECCION" "es" => array:2 [ "titulo" => "Comunicaciones breves" "idiomaDefecto" => true ] "idiomaDefecto" => "es" ] "PDF" => "https://static.elsevier.es/multimedia/00338338/0000004300000004/v1_201307311029/S003383380176955X/v1_201307311029/es/main.pdf?idApp=UINPBA00004N&text.app=https://www.elsevier.es/" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S003383380176955X?idApp=UINPBA00004N" ]
Información de la revista
Compartir
Descargar PDF
Más opciones de artículo
Síndrome de Noonan y quilotórax*
Noonan syndrome and chylothorax
María I. Martínez-León†
, Luisa Ceres-Ruiz, Ramón Solbes-Vila, Esperanza Valls-Moreno
Autor para correspondencia
Servicio de Radiodiagnóstico. Radiología Pediátrica. Hospital Materno-Infantil del C.H.U. «Carlos Haya». Málaga.