Información del artículo
Resumo
Recém-nascidos com Sequência de Robin frequentemente apresentam sérias obstruções respiratórias que podem representar riscos à vida resultante de malformações anatómicas (micrognatia, glossoptose e potenciais fendas palatinas). Esses pacientes precisam de medidas terapêuticas imediatas e efectivas. Dessa forma, o objectivo desse trabalho foi fazer uma revisão de literatura sobre a etiopatogenia, principais características e as actuais formas de tratamento empregadas para os portadores dessas alterações estruturais.
Palavras-Chave:
Síndrome de Pierre Robin
Fissura Palatina
Obstrução Vias Respiratórias
Abstract
Newborns with Pierre-Robin sequence often suffer from serious or even life-threatening obstructions in the respiratory tract resulting from anatomic malformations (micrognathia, glossoptosis and potentially a median cleft palate). Such babies require immediate effective therapeutic measures. Based on these facts, the aim of this article was to make a review of the literature about the etiopathogenesis, clinical characteristics and the current treatments for theses structural alterations.
Key-words:
Pierre Robin Syndrome
Cleft Palate
Airway Obstruction
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