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Inicio Acta Otorrinolaringológica Española Sarcoidosis laríngea aislada. a propósito de un caso
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Vol. 54. Issue 2.
Pages 117-120 (February 2003)
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Vol. 54. Issue 2.
Pages 117-120 (February 2003)
Sarcoidosis laríngea aislada. a propósito de un caso
Laryngeal Sarcoidosis: A Case Report
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P. Ezcurra Hernández1,*, A. Albertí I Casas*, E. Figuerola Massana*, S. Blázquez Vilá**, T. Sempere Durán***, F. Pellicer Garrido*, J. Risco Arenas*
* Servicio de otorrinolaringología
** Servicio de anatomía patológica
*** Servicio de radiodiagnóstico.Hospital universitari joan xxiii. Tarragona
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Resumen

La sarcoidosis es una enfermedad granulomatosa crónica multisistémica de etiología desconocida que afecta principalmente a adultos jóvenes. Se caracteriza por adenopatías hiliares bilaterales, infiltrado pulmonar intersticial, lesiones cutáneas y oculares. La afectación de la vía respiratoria superior es rara. Presentamos un caso clínico de un varón de 26 años que refiere sensación de cuerpo extraño en hipofaringe, disfonía y apneas obstructivas del sueño de tres meses de evolución debido a la infiltración de las estructuras supraglóticas por tejido sarcoideo. El diagnóstico se establece a partir de la clínica, los estudios radiológicos, las pruebas de laboratorio y el estudio histológico. El tratamiento de base son medidas de soporte, debido a la remisión espontánea de la clínica. Los corticoides sistémicos y locales presentan buenos resultados. En ocasiones son necesarias técnicas microquirúrgicas y la traqueotomía.

Palabras Clave:
Sarcoidosis en vía respiratoria superior
Apneas obstructivas del sueño
Reflujo gastroesofágico
Abstract

Sarcoidosis is a chronic multisystemic granulomatosis of unknown etiology that affects mainly young adults. It caracterized by bilateral hiliar adenopathies interstitial pulmonary infiltrate, and cutaneous and ocular lesions. Localization in upper respiratory tract is infrequent. In the present report we describe a 26-year-old male with a three-month history of a globus sensation, hoarse voice, loud snoring and obstructive sleep apnoea, because of a laryngeal noncaseating granulomatous infiltration. The diagnosis is made through the history, the radiology and the pathological examination. Treatment is symptomatic, due to its tendency to a spontaneous regression. The treatment is based on corticosteroids by systemic or aerosol routes. Micro surgical excision and tracheotomy may be useful in selected pat i e n t s.

Key Words:
Sarcoidosis
Upper respiratory tract
Obstructive sleep apnoea

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