array:23 [ "pii" => "S0210480603730198" "issn" => "02104806" "doi" => "10.1016/S0210-4806(03)73019-8" "estado" => "S300" "fechaPublicacion" => "2003-01-01" "aid" => "73019" "copyright" => "Asociación Española de Urología (AEU)" "copyrightAnyo" => "2003" "documento" => "article" "crossmark" => 0 "subdocumento" => "sco" "cita" => "Actas Urol Esp. 2003;27:809-13" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:2 [ "total" => 1040 "formatos" => array:3 [ "EPUB" => 5 "HTML" => 702 "PDF" => 333 ] ] "itemSiguiente" => array:18 [ "pii" => "S0210480603730204" "issn" => "02104806" "doi" => "10.1016/S0210-4806(03)73020-4" "estado" => "S300" "fechaPublicacion" => "2003-01-01" "aid" => "73020" "copyright" => "Asociación Española de Urología (AEU)" "documento" => "article" "crossmark" => 0 "subdocumento" => "sco" "cita" => "Actas Urol Esp. 2003;27:814-21" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:2 [ "total" => 1606 "formatos" => array:3 [ "EPUB" => 7 "HTML" => 959 "PDF" => 640 ] ] "es" => array:10 [ "idiomaDefecto" => true "titulo" => "Divertículo uretral femenino. a propósito de un caso" "tienePdf" => "es" "tieneTextoCompleto" => 0 "tieneResumen" => array:2 [ 0 => "es" 1 => "en" ] "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "814" "paginaFinal" => "821" ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "Female urethral diverticula. a propos of one case" ] ] "contieneResumen" => array:2 [ "es" => true "en" => true ] "contienePdf" => array:1 [ "es" => true ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "A. Gousse, M.F. Lorenzo-Gómez, L. Lebouef" "autores" => array:3 [ 0 => array:2 [ "nombre" => "A." "apellidos" => "Gousse" ] 1 => array:2 [ "nombre" => "M.F." "apellidos" => "Lorenzo-Gómez" ] 2 => array:2 [ "nombre" => "L." "apellidos" => "Lebouef" ] ] ] ] ] "idiomaDefecto" => "es" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0210480603730204?idApp=UINPBA00004N" "url" => "/02104806/0000002700000010/v1_201304251722/S0210480603730204/v1_201304251722/es/main.assets" ] "itemAnterior" => array:18 [ "pii" => "S0210480603730186" "issn" => "02104806" "doi" => "10.1016/S0210-4806(03)73018-6" "estado" => "S300" "fechaPublicacion" => "2003-01-01" "aid" => "73018" "copyright" => "Asociación Española de Urología (AEU)" "documento" => "article" "crossmark" => 0 "subdocumento" => "fla" "cita" => "Actas Urol Esp. 2003;27:803-8" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:2 [ "total" => 1755 "formatos" => array:3 [ "EPUB" => 7 "HTML" => 1130 "PDF" => 618 ] ] "es" => array:10 [ "idiomaDefecto" => true "titulo" => "Tratamiento con la técnica de nesbit en pacientes con la enfermedad de peyronie" "tienePdf" => "es" "tieneTextoCompleto" => 0 "tieneResumen" => array:2 [ 0 => "es" 1 => "en" ] "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "803" "paginaFinal" => "808" ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "Nesbit's technique treatment in patients with peyronie disease" ] ] "contieneResumen" => array:2 [ "es" => true "en" => true ] "contienePdf" => array:1 [ "es" => true ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "J. Rodríguez Tolrá, E. Franco Miranda, J.M. Prats Puig, O. Buisan Rueda, N. Serrallach Mila" "autores" => array:5 [ 0 => array:2 [ "nombre" => "J." "apellidos" => "Rodríguez Tolrá" ] 1 => array:2 [ "nombre" => "E." "apellidos" => "Franco Miranda" ] 2 => array:2 [ "nombre" => "J.M." "apellidos" => "Prats Puig" ] 3 => array:2 [ "nombre" => "O." "apellidos" => "Buisan Rueda" ] 4 => array:2 [ "nombre" => "N." "apellidos" => "Serrallach Mila" ] ] ] ] ] "idiomaDefecto" => "es" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0210480603730186?idApp=UINPBA00004N" "url" => "/02104806/0000002700000010/v1_201304251722/S0210480603730186/v1_201304251722/es/main.assets" ] "es" => array:13 [ "idiomaDefecto" => true "titulo" => "Nefroblastomatosis: ¿qué actitud terapéutica a seguir?. a propósito de 2 casos" "tieneTextoCompleto" => 0 "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "809" "paginaFinal" => "813" ] ] "autores" => array:1 [ 0 => array:4 [ "autoresLista" => "C. García Peñalver, F. López Vázquez, A. Gómez Fraile, A. Aransay Bramtot" "autores" => array:4 [ 0 => array:3 [ "nombre" => "C." "apellidos" => "García Peñalver" "referencia" => array:3 [ 0 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">*</span>" "identificador" => "aff0005" ] 1 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">1</span>" "identificador" => "cor0005" ] 2 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">a</span>" "identificador" => "aff0010" ] ] ] 1 => array:3 [ "nombre" => "F." "apellidos" => "López Vázquez" "referencia" => array:1 [ 0 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">a</span>" "identificador" => "aff0010" ] ] ] 2 => array:3 [ "nombre" => "A." "apellidos" => "Gómez Fraile" "referencia" => array:1 [ 0 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">a</span>" "identificador" => "aff0010" ] ] ] 3 => array:3 [ "nombre" => "A." "apellidos" => "Aransay Bramtot" "referencia" => array:1 [ 0 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">a</span>" "identificador" => "aff0010" ] ] ] ] "afiliaciones" => array:2 [ 0 => array:3 [ "entidad" => "Servicio de Urología. Hospital 12 de Octubre. Madrid" "etiqueta" => "<span class="elsevierStyleSup">*</span>" "identificador" => "aff0005" ] 1 => array:3 [ "entidad" => "Sección de Urología Pediátrica. Departamento de Cirugía Pediátrica. Servicio de Urología. Hospital 12 de Octubre. Madrid" "etiqueta" => "<span class="elsevierStyleSup">a</span>" "identificador" => "aff0010" ] ] "correspondencia" => array:1 [ 0 => array:3 [ "identificador" => "cor0005" "etiqueta" => "1" "correspondencia" => "Dr. C. García Peñalver C/ Baldomero Díaz Entresoto, 1 - 2º C 06800 Mérida (Badajoz)" ] ] ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "What is the appropriate therapeutic approach to nephroblastomatosis? a report of 2 cases" ] ] "pdfFichero" => "main.pdf" "tienePdf" => true "fechaRecibido" => "2003-03-21" "PalabrasClave" => array:2 [ "es" => array:1 [ 0 => array:4 [ "clase" => "keyword" "titulo" => "Palabras clave" "identificador" => "xpalclavsec87031" "palabras" => array:3 [ 0 => "Restos nefrogénicos" 1 => "Nefroblastomatosis" 2 => "Tumor de Wilms" ] ] ] "en" => array:1 [ 0 => array:4 [ "clase" => "keyword" "titulo" => "Key words" "identificador" => "xpalclavsec87032" "palabras" => array:3 [ 0 => "Nephrogenic rests" 1 => "Nephroblastomatosis" 2 => "Wilm's tumor" ] ] ] ] "tieneResumen" => true "resumen" => array:2 [ "es" => array:2 [ "titulo" => "Resumen" "resumen" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">La nefroblastomatosis representa un complejo de entidades patológicas definidas por la persistencia de elementos nefrogénicos tras la nefrogénesis (más allá de la 36 semana de gestación), los cuales conservan la capacidad de evolución hacia nefroblastoma. Afortunadamente, esta transformación maligna ocurre excepcionalmete (<1%1), por lo que es considerada como una enfermedad de buen pronóstico. Los restos nefrogénicos se asocian con frecuencia al Sd. de Beckwith- Wiedemann, a la hemihipertrofia y la aniridia, teniendo en tales casos un riesgo mayor de desarrollar un tumor de Wilms, por lo que estos niños deben ser seguidos muy de cerca. El problema se nos plantea a la hora de decidir cuándo actuar, a qué niños tratar y qué tipo de tratamiento utilizar, pues lo poco publicado en la literatura se presta a discusión. Presentamos a continuación 2 casos de nefroblastomatosis, uno unilateral y otro bilateral que precisó de tratamiento quirúrgico al no responder a la quimioterapia.</p>" ] "en" => array:2 [ "titulo" => "Abstract" "resumen" => "<p id="spar0010" class="elsevierStyleSimplePara elsevierViewall">Nephroblastomatosis is a complex of pathological conditions defined by the persistence of nephrogenic elements after the conclusion of nephrogenesis (beyond week 36 of gestation) that conserve the capacity to evolve into nephroblastoma. Luckily, this malignant transformation is exceptional (<1%1), which is why the disease is considered to have a good prognosis. The nephrogenic remains are frequently associated with Beckwith-Wiedemann syndrome, hemihypertrophy and aniridia, in which case there is a greater risk of the development of Wilms tumor. Consequently, these children must be followed-up closely. The difficulty lay in knowing when to act, which children should be treated, and what treatment is appropriate because what little has been published in the literature is debatable. We report the cases of two patients, one with unilateral nephroblastomatosis and the other bilateral, who required surgical treatment after not responding to chemotherapy; and we expose our therapeutic algorithm and follow-up strategy.</p>" ] ] "bibliografia" => array:2 [ "titulo" => "Referencias" "seccion" => array:1 [ 0 => array:2 [ "identificador" => "bibs0005" "bibliografiaReferencia" => array:8 [ 0 => array:3 [ "identificador" => "bib0005" "etiqueta" => "1." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Nephrogenic rests and the pathogenesis of wilms´ tumor: developmental clinical considerations" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:1 [ 0 => "J.B. Beckwith" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Am J Med Genet" "fecha" => "1998" "volumen" => "79" "paginaInicial" => "268" "paginaFinal" => "273" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9781906" "web" => "Medline" ] ] ] ] ] ] ] ] 1 => array:3 [ "identificador" => "bib0010" "etiqueta" => "2." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Nephrogenic rests, nephroblastomatosis, and the pathogenesis of wilms' tumor" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:3 [ 0 => "J.B. Beckwith" 1 => "N.B. Kiviat" 2 => "J.F. Bonadio" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Pediatr Pathol" "fecha" => "1990" "volumen" => "10" "paginaInicial" => "1" "paginaFinal" => "36" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/2156243" "web" => "Medline" ] ] ] ] ] ] ] ] 2 => array:3 [ "identificador" => "bib0015" "etiqueta" => "3." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Nephrogenic rests, nephroblastomatosis, and associated lesions of the kidney" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:3 [ 0 => "G.J. Lonergan" 1 => "M.I. Martínez-león" 2 => "G.A. Agrons" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1148/radiographics.18.4.9672980" "Revista" => array:7 [ "tituloSerie" => "Radiographics" "fecha" => "1998" "volumen" => "18" "numero" => "4" "paginaInicial" => "947" "paginaFinal" => "968" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9672980" "web" => "Medline" ] ] ] ] ] ] ] ] 3 => array:3 [ "identificador" => "bib0020" "etiqueta" => "4." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Screening for wilms tumors in high-risks individuals" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "C.L. Clericuzio" 1 => "C. Jonson" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Hematol Oncol Clin North Am" "fecha" => "1995" "volumen" => "9" "paginaInicial" => "1253" "paginaFinal" => "1265" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/8591963" "web" => "Medline" ] ] ] ] ] ] ] ] 4 => array:3 [ "identificador" => "bib0025" "etiqueta" => "5." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "US, ct and mr imaging characteristics of nephroblastomatosis" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:3 [ 0 => "W.K. Rohrschneider" 1 => "A. Weirich" 2 => "K. Rieden" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1007/s002470050378" "Revista" => array:6 [ "tituloSerie" => "Pediatr Radiol" "fecha" => "1998" "volumen" => "28" "paginaInicial" => "435" "paginaFinal" => "443" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9634458" "web" => "Medline" ] ] ] ] ] ] ] ] 5 => array:3 [ "identificador" => "bib0030" "etiqueta" => "6." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Management decisions in children with nephroblastomatosis" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:3 [ 0 => "P. Prasil" 1 => "J.M. Laderge" 2 => "M. Bond" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:7 [ "tituloSerie" => "Med Pediatr Oncol" "fecha" => "2000" "volumen" => "35" "numero" => "4" "paginaInicial" => "429" "paginaFinal" => "432" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/11025476" "web" => "Medline" ] ] ] ] ] ] ] ] 6 => array:3 [ "identificador" => "bib0035" "etiqueta" => "7." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "New developments in the pathology of wilms' tumor" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:1 [ 0 => "J.B. Beckwith" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Cancer Invest" "fecha" => "1997" "volumen" => "15" "paginaInicial" => "153" "paginaFinal" => "162" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9095211" "web" => "Medline" ] ] ] ] ] ] ] ] 7 => array:3 [ "identificador" => "bib0040" "etiqueta" => "8." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "The role of preoperative chemotherapy in the management of wilm´s tumor. the siop studies. international society of pediatric oncology" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "N. Graf" 1 => "M.F. Tournade" 2 => "J. De-kraker" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:7 [ "tituloSerie" => "Urol Clin North Am" "fecha" => "2000" "volumen" => "27" "numero" => "3" "paginaInicial" => "443" "paginaFinal" => "454" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/10985144" "web" => "Medline" ] ] ] ] ] ] ] ] ] ] ] ] ] "idiomaDefecto" => "es" "url" => "/02104806/0000002700000010/v1_201304251722/S0210480603730198/v1_201304251722/es/main.assets" "Apartado" => array:4 [ "identificador" => "6431" "tipo" => "SECCION" "es" => array:2 [ "titulo" => "Nota clínica" "idiomaDefecto" => true ] "idiomaDefecto" => "es" ] "PDF" => "https://static.elsevier.es/multimedia/02104806/0000002700000010/v1_201304251722/S0210480603730198/v1_201304251722/es/main.pdf?idApp=UINPBA00004N&text.app=https://www.elsevier.es/" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0210480603730198?idApp=UINPBA00004N" ]
Journal Information
Nefroblastomatosis: ¿qué actitud terapéutica a seguir?. a propósito de 2 casos
What is the appropriate therapeutic approach to nephroblastomatosis? a report of 2 cases