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Funduscopy of the right eye showed mild vitreous haemorrhage and several peripheral capillary haemangiomas (<a class="elsevierStyleCrossRef" href="#fig0005">Fig. 1</a>). An exploration of the left eye was normal. When Von Hippel-Lindau disease was suspected, imaging tests were ordered and cystic lesions were detected in several visceral organs, with two cerebellar haemangiomas (<a class="elsevierStyleCrossRef" href="#fig0010">Fig. 2</a>). The genetic study was positive for Von Hippel-Lindau disease.</p><elsevierMultimedia ident="fig0005"></elsevierMultimedia><elsevierMultimedia ident="fig0010"></elsevierMultimedia><p id="par0010" class="elsevierStylePara elsevierViewall">The capillary haemangioma of the retina is a retinal vascular tumour that can appear in isolation, although half of the subjects with isolated haemangiomas and practically all patients with multiple lesions have Von Hippel-Lindau disease. Performing a systemic study to rule out involvement of other organs is mandatory once it is discovered. It is important to highlight the central nervous system involvement, since it is be present in up to 25% of cases with retinal haemangiomas.</p></span>" "pdfFichero" => "main.pdf" "tienePdf" => true "NotaPie" => array:1 [ 0 => array:2 [ "etiqueta" => "☆" "nota" => "<p class="elsevierStyleNotepara" id="npar0005">Please cite this article as: Ramos Suárez A, Alfaro Juárez AM, Sánchez Merino C. Hemangioma capilar retiniano y enfermedad de Von Hippel-Lindau. 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Image in medicine
Retinal capillary hemangioma and von Hippel-Lindau disease
Hemangioma capilar retiniano y enfermedad de Von Hippel-Lindau
Antonio Ramos Suárez
, Ana María Alfaro Juárez, Carlos Sánchez Merino
Corresponding author
Servicio de Oftalmología, Hospital General Básico de Baza, Baza, Granada, Spain