Diagnosis by multimodal imaging in peripapillary pachychoroid syndrome: A case report

Abstract

The case is reported of a 73-year-old male presenting with the recently described peripapillary pachychoroid syndrome. This syndrome is included in the pachychoroid diseases, which is a relatively new condition characterized by increased choroidal thickness with attenuation of the choriocapillary layer located above dilated choroidal vessels. It is associated with progressive malfunction of the retinal pigment epithelium and neovascularisation. The case is presented with a multimodal image, in which some tests show signs not previously described. In addition, a description is presented of the asymmetric outcome of both eyes after multiple treatments, since the left eye has a very severe affectation, and is refractory to the treatment.

Resumen

Se presenta el caso de un varón de 73 años con el recientemente descrito síndrome paquicoroideo peripapilar. Este síndrome se incluye dentro de las enfermedades paquicoroideas, que constituyen una entidad relativamente novedosa caracterizada por un aumento del grosor coroideo con atenuación de la capa coriocapilar situada por encima de vasos coroideos dilatados. Asocia mal funcionamiento progresivo del epitelio pigmentario retiniano junto con neovascularización. Se presenta el caso con imagen multimodal, en la que algunas pruebas muestran signos no descritos previamente. Además, se describe la evolución asimétrica de ambos ojos tras múltiples tratamientos, ya que el ojo izquierdo presenta una afectación muy severa y refractaria al tratamiento.