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Exploración física y analítica sin alteraciones significativas. La TC abdominal, RMN (<a class="elsevierStyleCrossRef" href="#fig0005">fig. 1</a>) y Doppler hepático, identifican una gran dilatación varicosa de la vena mesentérica inferior (VMI) con <span class="elsevierStyleItalic">shunt</span> mesentérico-hipogástrico. La gran VMI (<a class="elsevierStyleCrossRef" href="#fig0005">fig. 1</a>) muestra flujo invertido y no hay ramas portales intra ni extrahepáticas. La malformación de Abernethy es la ausencia congénita de vena porta con <span class="elsevierStyleItalic">shunt</span> cavo-mesentérico secundario. Existen 2 tipos: <span class="elsevierStyleSmallCaps">I</span>: <span class="elsevierStyleItalic">Shunt</span> término-lateral (ausencia total de flujo portal intrahepático) y <span class="elsevierStyleSmallCaps">II</span>: <span class="elsevierStyleItalic">Shunt</span> latero-lateral (flujo portal parcialmente conservado).</p><elsevierMultimedia ident="fig0005"></elsevierMultimedia><p id="par0010" class="elsevierStylePara elsevierViewall">Diagnóstico: Malformación de Abernethy.</p></span>" "pdfFichero" => "main.pdf" "tienePdf" => true "multimedia" => array:1 [ 0 => array:6 [ "identificador" => "fig0005" "etiqueta" => "Figura 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 1378 "Ancho" => 1667 "Tamanyo" => 139647 ] ] ] ] ] "idiomaDefecto" => "es" "url" => "/0009739X/0000009300000003/v2_201502230146/S0009739X14003418/v2_201502230146/es/main.assets" "Apartado" => array:4 [ "identificador" => "15025" "tipo" => "SECCION" "es" => array:2 [ "titulo" => "La imagen del mes" "idiomaDefecto" => true ] "idiomaDefecto" => "es" ] "PDF" => "https://static.elsevier.es/multimedia/0009739X/0000009300000003/v2_201502230146/S0009739X14003418/v2_201502230146/es/main.pdf?idApp=UINPBA00004N&text.app=https://www.elsevier.es/" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0009739X14003418?idApp=UINPBA00004N" ]
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Malformación de Abernethy: shunt portosistémico congénito
Abernethy malformation: Congenital portosystemic shunt
Fernanda Benavides de la Rosa
, Íñigo López de Cenarruzabeitia, Juan García-Castaño Gandiaga, Juan Pablo Beltrán de Heredia
Autor para correspondencia
Servicio de Cirugía General y del Aparato Digestivo, Hospital Clínico Universitario de Valladolid, Valladolid, España
Artículo
Este artículo está disponible en español
Malformación de Abernethy: shunt portosistémico congénito
Fernanda Benavides de la Rosa, Íñigo López de Cenarruzabeitia, Juan García-Castaño Gandiaga, Juan Pablo Beltrán de Heredia
10.1016/j.ciresp.2014.10.012Cir Esp. 2015;93:e17
This article is available in English
Abernethy Malformation: Congenital Porthosystemic Shunt
Fernanda Benavides de la Rosa, Íñigo López de Cenarruzabeitia, Juan García-Castaño Gandiaga, Juan Pablo Beltrán de Heredia
10.1016/j.cireng.2014.10.003Cir Esp. 2015;93:e17