Información del artículo
Resumen
Se presenta el caso de una mujer de 16 años de edad, con síndrome de Alagille, que presentó una hemorragia digestiva por rotura de varices esofágicas secundarias a una hipertensión portal presinusoidal por trombosis portal, sin evidencia de fibrosis hepática, fenómeno no descrito con anterioridad en este síndrome.
We present the case of a 16-year old woman with Alagille's syndrome, who had upper gastrointestinal bleeding due to rupture of esophageal varices secondary to presinusoidal portal hypertension without liver fibrosis. Portal thrombosis is a manifestation previously unreported in association to this syndrome.
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