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Inicio Gastroenterología y Hepatología Síndrome de Ehlers-Danlos asociado a pancreatitis aguda
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Vol. 24. Núm. 1.
Páginas 13-15 (enero 2001)
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Vol. 24. Núm. 1.
Páginas 13-15 (enero 2001)
Acceso a texto completo
Síndrome de Ehlers-Danlos asociado a pancreatitis aguda
Ehlers-danlos syndrome associated with acute pancreatitis
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A. Indart*,1, L.F. Alzate1, J.I. Arenas1, P. Zugastia
1 Servicios de Aparato Digestivo Hospital de Aránzazu. San Sebastián
a Servicios de Aparato Digestivo Cirugía General. Hospital de Aránzazu. San Sebastián
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Resumen

El síndrome de Ehlers-Danlos es una enfermedad congénita del tejido conectivo caracterizada por laxitud articular, hiperelasticidad de la piel y fragilidad tisular. Este síndrome se caracteriza por su gran heterogeneidad clínica, genética y bioquímica, y han sido descritos varios subtipos. Describimos el caso de un paciente con la variante IV de este síndrome que desarrolló una pancreatitis aguda de forma espontánea.

Abstract

Ehlers-Danlos syndrome is an inherited connective tissue disease characterized by articular laxity, hyperelastic skin and tissue fragility. The syndrome is genetically, biochemically and clinically heterogeneous and several well-defined subtypes have been identified. We describe a patient with the type IV variant of this syndrome who developed acute spontaneous pancreatitis.

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Copyright © 2001. Elsevier España, S.L.. Todos los derechos reservados
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