Artículo
Comprando el artículo el PDF del mismo podrá ser descargado
Precio 19,34 €
Comprar ahora
array:23 [ "pii" => "S2387020620306562" "issn" => "23870206" "doi" => "10.1016/j.medcle.2019.11.017" "estado" => "S300" "fechaPublicacion" => "2021-02-12" "aid" => "5084" "copyright" => "Elsevier España, S.L.U.. All rights reserved" "copyrightAnyo" => "2020" "documento" => "simple-article" "crossmark" => 1 "subdocumento" => "cor" "cita" => "Med Clin. 2021;156:151-2" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:1 [ "total" => 0 ] "itemSiguiente" => array:19 [ "pii" => "S238702062030646X" "issn" => "23870206" "doi" => "10.1016/j.medcle.2019.11.016" "estado" => "S300" "fechaPublicacion" => "2021-02-12" "aid" => "5079" "copyright" => "Elsevier España, S.L.U." "documento" => "article" "crossmark" => 1 "subdocumento" => "sco" "cita" => "Med Clin. 2021;156:153" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:1 [ "total" => 0 ] "en" => array:11 [ "idiomaDefecto" => true "cabecera" => "<span class="elsevierStyleTextfn">Image in medicine</span>" "titulo" => "Phototoxic reaction caused by contact with topic ketoprofen" "tienePdf" => "en" "tieneTextoCompleto" => "en" "paginas" => array:1 [ 0 => array:1 [ "paginaInicial" => "153" ] ] "titulosAlternativos" => array:1 [ "es" => array:1 [ "titulo" => "Reacción fototóxica causada por contacto con ketoprofeno tópico" ] ] "contieneTextoCompleto" => array:1 [ "en" => true ] "contienePdf" => array:1 [ "en" => true ] "resumenGrafico" => array:2 [ "original" => 0 "multimedia" => array:6 [ "identificador" => "fig0005" "etiqueta" => "Figure 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 1205 "Ancho" => 905 "Tamanyo" => 252839 ] ] ] ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "Elisabeth Gómez Moyano, Jesica Martín Carmona, Ricardo Gómez Huelgas, Leandro Martínez Pilar" "autores" => array:4 [ 0 => array:2 [ "nombre" => "Elisabeth" "apellidos" => "Gómez Moyano" ] 1 => array:2 [ "nombre" => "Jesica" "apellidos" => "Martín Carmona" ] 2 => array:2 [ "nombre" => "Ricardo" "apellidos" => "Gómez Huelgas" ] 3 => array:2 [ "nombre" => "Leandro" "apellidos" => "Martínez Pilar" ] ] ] ] ] "idiomaDefecto" => "en" "Traduccion" => array:1 [ "es" => array:9 [ "pii" => "S0025775320300956" "doi" => "10.1016/j.medcli.2019.11.013" "estado" => "S300" "subdocumento" => "" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:1 [ "total" => 0 ] "idiomaDefecto" => "es" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0025775320300956?idApp=UINPBA00004N" ] ] "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S238702062030646X?idApp=UINPBA00004N" "url" => "/23870206/0000015600000003/v1_202102051000/S238702062030646X/v1_202102051000/en/main.assets" ] "itemAnterior" => array:18 [ "pii" => "S2387020620306574" "issn" => "23870206" "doi" => "10.1016/j.medcle.2019.10.028" "estado" => "S300" "fechaPublicacion" => "2021-02-12" "aid" => "5122" "copyright" => "Elsevier España, S.L.U." "documento" => "simple-article" "crossmark" => 1 "subdocumento" => "cor" "cita" => "Med Clin. 2021;156:150-1" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:1 [ "total" => 0 ] "en" => array:10 [ "idiomaDefecto" => true "cabecera" => "<span class="elsevierStyleTextfn">Letter to the Editor</span>" "titulo" => "Reply to “To improve in diagnostic safety: The pending subject”" "tienePdf" => "en" "tieneTextoCompleto" => "en" "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "150" "paginaFinal" => "151" ] ] "titulosAlternativos" => array:1 [ "es" => array:1 [ "titulo" => "En respuesta a “Mejorar en seguridad diagnóstica: la asignatura pendiente”" ] ] "contieneTextoCompleto" => array:1 [ "en" => true ] "contienePdf" => array:1 [ "en" => true ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "Joao Luis Modesto Dos Santos, Beatriz Zabalza Ollo, Susana Clemos Matamoros" "autores" => array:3 [ 0 => array:2 [ "nombre" => "Joao Luis" "apellidos" => "Modesto Dos Santos" ] 1 => array:2 [ "nombre" => "Beatriz" "apellidos" => "Zabalza Ollo" ] 2 => array:2 [ "nombre" => "Susana" "apellidos" => "Clemos Matamoros" ] ] ] ] ] "idiomaDefecto" => "en" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S2387020620306574?idApp=UINPBA00004N" "url" => "/23870206/0000015600000003/v1_202102051000/S2387020620306574/v1_202102051000/en/main.assets" ] "en" => array:15 [ "idiomaDefecto" => true "cabecera" => "<span class="elsevierStyleTextfn">Letter to the Editor</span>" "titulo" => "Cardiac dextroposition associated to Poland syndrome" "tieneTextoCompleto" => true "saludo" => "Dear Editor," "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "151" "paginaFinal" => "152" ] ] "autores" => array:1 [ 0 => array:4 [ "autoresLista" => "Elena Guadalupe Corella Aznar, Ariadna Ayerza Casas, Daniel Palanca Arias, Lorenzo Jiménez Montañés" "autores" => array:4 [ 0 => array:4 [ "nombre" => "Elena Guadalupe" "apellidos" => "Corella Aznar" "email" => array:1 [ 0 => "elena_corella88@hotmail.com" ] "referencia" => array:1 [ 0 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">*</span>" "identificador" => "cor0005" ] ] ] 1 => array:2 [ "nombre" => "Ariadna" "apellidos" => "Ayerza Casas" ] 2 => array:2 [ "nombre" => "Daniel" "apellidos" => "Palanca Arias" ] 3 => array:2 [ "nombre" => "Lorenzo" "apellidos" => "Jiménez Montañés" ] ] "afiliaciones" => array:1 [ 0 => array:2 [ "entidad" => "Unidad Cardiologia Pediátrica, Hospital Infantil Miguel Servet, Zaragoza, Spain" "identificador" => "aff0005" ] ] "correspondencia" => array:1 [ 0 => array:3 [ "identificador" => "cor0005" "etiqueta" => "⁎" "correspondencia" => "Corresponding author." ] ] ] ] "titulosAlternativos" => array:1 [ "es" => array:1 [ "titulo" => "Síndrome de Poland asociado a dextrocardia" ] ] "resumenGrafico" => array:2 [ "original" => 0 "multimedia" => array:7 [ "identificador" => "fig0005" "etiqueta" => "Fig. 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 548 "Ancho" => 1255 "Tamanyo" => 72376 ] ] "descripcion" => array:1 [ "en" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">(A) Chest X-rays demonstrated an isolated dextrocardia (*), with an asymmetric thorax but without ribs defects. Pulmonary anatomy seems to be normal, with right lobar bronchi on the right and two on the left; the gastric bubble was on the left side (arrow), and liver on the right side (+). (B) Depression of the left anterior chest wall and nipple defect (arrows).</p>" ] ] ] "textoCompleto" => "<span class="elsevierStyleSections"><p id="par0005" class="elsevierStylePara elsevierViewall">Poland syndrome is a rare congenital disorder characterized by aplasia or hypoplasia of the ipsilateral chest muscles, major and minor pectoralis, associated with abnormalities of the hand, such as brachydactyly, syndactyly or underdeveloped (vestigial) fingers.<a class="elsevierStyleCrossRefs" href="#bib0030"><span class="elsevierStyleSup">1,2</span></a> This clinical manifestations are extremely variable; breast and nipple abnormalities may also occur, and axillary hair is sometimes sparse or abnormally placed. Other very rares anomalies like vertebral defects, renal aplasia or hypoplasia, lower limbs defects or Möbius syndrome can be associated.<a class="elsevierStyleCrossRef" href="#bib0040"><span class="elsevierStyleSup">3</span></a> Rarely all of these features are recognized in the same patient.<a class="elsevierStyleCrossRef" href="#bib0045"><span class="elsevierStyleSup">4</span></a></p><p id="par0010" class="elsevierStylePara elsevierViewall">This syndrome has been estimated to occur in 1:20,000 to 1:30,000 newborns, and it is more common in male than in female individuals, and also more frequent on the right side.<a class="elsevierStyleCrossRef" href="#bib0040"><span class="elsevierStyleSup">3</span></a></p><p id="par0015" class="elsevierStylePara elsevierViewall">The cause of the Poland syndrome remain still unkown, however some reports suggest that it may result from a disruption of blood flow (of the subclavian and vertebral arteries) during the sixth week of gestation.<a class="elsevierStyleCrossRef" href="#bib0030"><span class="elsevierStyleSup">1</span></a> But it is also thought that a possible genetic inheritance could be related, however no genes have been identified.</p><p id="par0020" class="elsevierStylePara elsevierViewall">Differential diagnosis of dextrocardia with sinus solitus must included syndromes such as Scimitar syndrome and Cantrell's syndrome, which is characterized by defects of the midline abdominal wall. But none of them are associated with hypoplasia or agenesia of pectoralis muscle, which is specific of Poland syndrome.</p><p id="par0025" class="elsevierStylePara elsevierViewall">We present a case of 18 months-old male, with no relevant anomalies in the family was referred to the Pediatric Cardiologist because of a dextrocardia in the radiological examination. The chest X-ray demonstrated an isolated dextrocardia (<a class="elsevierStyleCrossRef" href="#fig0005">Fig. 1</a>A), with an asymmetric thorax but without ribs defects, and normal abdominal organs arrangement.</p><elsevierMultimedia ident="fig0005"></elsevierMultimedia><p id="par0030" class="elsevierStylePara elsevierViewall">The ecocardiography revealed a displacement of the heart's large axis to the right side with the heart apex in the midline of the thorax (mesocardia), and a left aortic arch. No evidence of intracardiac malformations, neither alteration of the grand vessels anomalies were seen.</p><p id="par0035" class="elsevierStylePara elsevierViewall">The physical exam showed a smaller left areola, also located slightly higher than the right one. Also a hypoplasia of subcutneous tissue on the left wall chest could be noted, which suggested a defect in the left pectoralis muscle (<a class="elsevierStyleCrossRef" href="#fig0005">Fig. 1</a>B). But there were no evidence of an associated syndactylism or brachysyndactyly anomaly.</p><p id="par0040" class="elsevierStylePara elsevierViewall">Clinically, patient did not show any functional disability, neither deficiencies in muscle strength. Further systemic examinations were carried out, excluding renal anomalies.</p><p id="par0045" class="elsevierStylePara elsevierViewall">Regarding to the treatment, conservative management was chosen with physical therapy, which may be beneficial in improving strength and mobility. In the future, reconstructive surgery may be considered to develop symmetry between the affected and unaffected side.</p><p id="par0050" class="elsevierStylePara elsevierViewall">Left-sided Poland syndrome is uncommon, but mainly its association with dextrocardia is extremely rare. To date, only 14 cases with similar characteristics have been described.</p><p id="par0055" class="elsevierStylePara elsevierViewall">Our patient as well as having a malformation of the left pectoralis muscle, showed a morphological normal heart displaced to the right side of the chest. This finding called dextroposition, has an incidence which varies from 30,000 to 1 in 36,000 newborns<a class="elsevierStyleCrossRef" href="#bib0050"><span class="elsevierStyleSup">5</span></a> and it can be presented as part of situs inversus (heterotaxia), or an isolated situs solitus defect.</p><p id="par0060" class="elsevierStylePara elsevierViewall">Because both isolated dextroposition and Poland syndrome are very rare, we believe that the relationship between dextrocardia and PS is not a coincidence, whereas dextroposition may be part of the Poland syndrome, especially left-sided.</p><p id="par0065" class="elsevierStylePara elsevierViewall">Moreover, every Polar syndrome with dextrocardia reported had associated any rib defect. Different from these reported cases, our patient did not show any rib abnormality, which shows that is not necessary any rib defect to displace the heart.</p><span id="sec0005" class="elsevierStyleSection elsevierViewall"><span class="elsevierStyleSectionTitle" id="sect0005">Funding</span><p id="par0070" class="elsevierStylePara elsevierViewall">This research received no specific grant from any funding agency, commercial or not-for-profit sectors.</p></span><span id="sec0010" class="elsevierStyleSection elsevierViewall"><span class="elsevierStyleSectionTitle" id="sect0010">Conflicts of interest</span><p id="par0075" class="elsevierStylePara elsevierViewall">None.</p></span></span>" "textoCompletoSecciones" => array:1 [ "secciones" => array:3 [ 0 => array:2 [ "identificador" => "sec0005" "titulo" => "Funding" ] 1 => array:2 [ "identificador" => "sec0010" "titulo" => "Conflicts of interest" ] 2 => array:1 [ "titulo" => "References" ] ] ] "pdfFichero" => "main.pdf" "tienePdf" => true "multimedia" => array:1 [ 0 => array:7 [ "identificador" => "fig0005" "etiqueta" => "Fig. 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 548 "Ancho" => 1255 "Tamanyo" => 72376 ] ] "descripcion" => array:1 [ "en" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">(A) Chest X-rays demonstrated an isolated dextrocardia (*), with an asymmetric thorax but without ribs defects. Pulmonary anatomy seems to be normal, with right lobar bronchi on the right and two on the left; the gastric bubble was on the left side (arrow), and liver on the right side (+). (B) Depression of the left anterior chest wall and nipple defect (arrows).</p>" ] ] ] "bibliografia" => array:2 [ "titulo" => "References" "seccion" => array:1 [ 0 => array:2 [ "identificador" => "bibs0015" "bibliografiaReferencia" => array:5 [ 0 => array:3 [ "identificador" => "bib0030" "etiqueta" => "1" "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Dextrocardia in patients with Poland syndrome: phenotypic characterization provides insight into the pathogenesis" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:6 [ 0 => "M. Torre" 1 => "A. Baban" 2 => "A. Buluggiu" 3 => "S. Constanzo" 4 => "L. Bricco" 5 => "M. Lerone" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "J Thorac Cardiovasc Surg" "fecha" => "2010" "volumen" => "1395" "paginaInicial" => "1177" "paginaFinal" => "1182" ] ] ] ] ] ] 1 => array:3 [ "identificador" => "bib0035" "etiqueta" => "2" "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Poland syndrome: description of an atypical variant" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:4 [ 0 => "G.A. Ferraro" 1 => "A. Perrotta" 2 => "F. Rossano" 3 => "F. D’Andrea" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "Aesth Plast Surg" "fecha" => "2005" "volumen" => "29" "paginaInicial" => "32" "paginaFinal" => "33" ] ] ] ] ] ] 2 => array:3 [ "identificador" => "bib0040" "etiqueta" => "3" "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Poland's syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "C.R. Moir" 1 => "C.H. Johnson" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1053/j.sempedsurg.2008.03.005" "Revista" => array:6 [ "tituloSerie" => "Semin Pediatr Surg" "fecha" => "2008" "volumen" => "17" "paginaInicial" => "161" "paginaFinal" => "166" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/18582821" "web" => "Medline" ] ] ] ] ] ] ] ] 3 => array:3 [ "identificador" => "bib0045" "etiqueta" => "4" "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "A case of Poland syndrome associated with dextroposition" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "D. Lacorte" 1 => "M. Marsella" 2 => "P. Guerrini" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1186/1824-7288-36-21" "Revista" => array:5 [ "tituloSerie" => "Ital J Pediatr" "fecha" => "2010" "volumen" => "36" "paginaInicial" => "21" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/20170539" "web" => "Medline" ] ] ] ] ] ] ] ] 4 => array:3 [ "identificador" => "bib0050" "etiqueta" => "5" "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Poland's syndrome revisited" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "A.A. Fokin" 1 => "F. Robicsek" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1016/s0003-4975(02)04161-9" "Revista" => array:6 [ "tituloSerie" => "Ann Thorac Surg" "fecha" => "2002" "volumen" => "74" "paginaInicial" => "2218" "paginaFinal" => "2225" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/12643435" "web" => "Medline" ] ] ] ] ] ] ] ] ] ] ] ] ] "idiomaDefecto" => "en" "url" => "/23870206/0000015600000003/v1_202102051000/S2387020620306562/v1_202102051000/en/main.assets" "Apartado" => array:4 [ "identificador" => "43309" "tipo" => "SECCION" "en" => array:2 [ "titulo" => "Letters to the Editor" "idiomaDefecto" => true ] "idiomaDefecto" => "en" ] "PDF" => "https://static.elsevier.es/multimedia/23870206/0000015600000003/v1_202102051000/S2387020620306562/v1_202102051000/en/main.pdf?idApp=UINPBA00004N&text.app=https://www.elsevier.es/" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S2387020620306562?idApp=UINPBA00004N" ]
Consulte los artículos y contenidos publicados en este medio, además de los e-sumarios de las revistas científicas en el mismo momento de publicación
Esté informado en todo momento gracias a las alertas y novedades
Acceda a promociones exclusivas en suscripciones, lanzamientos y cursos acreditados
Launched in 1943, Medicina Clínica is a fortnightly journal aimed at the promotion of clinical research and practice among internal medicine and other specialists. The key characteristics of Medicina Clínica are the scientific and methodological rigor of its manuscripts, the topicality of its contents, and, especially, its practical focus with highly useful information for clinical practice. Medicina Clínica is predominantly interested in publishing original research manuscripts, which are rigorously selected according to their quality, originality, and interest, and also in continued medical education-oriented manuscripts, which are commissioned by the journal to relevant authors (Editorials, Reviews, and Diagnosis and Treatment). These manuscripts contain updated topics with a major clinical or conceptual relevance in modern medicine. The journal adheres to the standards of academic research publications in all aspects including peer-review and ethical principles. Medicina Clínica is included in the General and Internal Medicine category of Thomson Reuters.
Current Contents/Clinical Medicine, Journal Citation Reports, SCI-Expanded, Index Medicus/Medline, Excerpta Medica/EMBASE, IBECS, IME, MEDES, PASCAL, SCOPUS, SciVerse ScienceDirect
Ver másEl factor de impacto mide la media del número de citaciones recibidas en un año por trabajos publicados en la publicación durante los dos años anteriores.
© Clarivate Analytics, Journal Citation Reports 2022
SJR es una prestigiosa métrica basada en la idea de que todas las citaciones no son iguales. SJR usa un algoritmo similar al page rank de Google; es una medida cuantitativa y cualitativa al impacto de una publicación.
Ver másSNIP permite comparar el impacto de revistas de diferentes campos temáticos, corrigiendo las diferencias en la probabilidad de ser citado que existe entre revistas de distintas materias.
Ver másMedicina Clínica (English Edition) sigue las recomendaciones para la preparación, presentación y publicación de trabajos académicos en revistas biomédicas
¿Es usted profesional sanitario apto para prescribir o dispensar medicamentos?
Are you a health professional able to prescribe or dispense drugs?
Você é um profissional de saúde habilitado a prescrever ou dispensar medicamentos