Scleromyxoedema with extracutaneous pulmonary manifestation: A case report and review of the literature

Bedoya-Joaqui, Vanessa; Varela-Muñoz, María J.; Parra-Lara, Luis G.; Garzón-Portilla, María C.; Muñoz, Liliana; Aguirre-Valencia, David A.

doi:10.1016/j.rcreue.2024.02.001

ISSN: 2444-4405

The Colombian Journal of Rheumatology (Revista Colombiana de Reumatología) is the official organ of the Colombian Association of Rheumatology (Asociación Colombiana de Reumatología) and the Central American, Caribbean and Andean Association of Rheumatology (Asociación Centroamericana Caribe Andina de Reumatología) - ACCAR. It was created in December 1993 with the purpose of disseminating scientific information derived from primary and secondary research and presenting cases coming from the practice of Rheumatology in Latin America. Since its foundation, the Journal has been characterized by its plurality with subjects of all rheumatic and osteomuscular pathologies, in the form of original articles, historical articles, economic evaluations, and articles of reflection and education in Medicine. It covers an extensive area of topics ranging from the broad spectrum of the clinical aspects of rheumatology and related areas in autoimmunity (both in pediatric and adult pathologies), to aspects of basic sciences. It is an academic tool for the different members of the academic and scientific community at their different levels of training, from undergraduate to post-doctoral degrees, managing to integrate all actors inter-and transdisciplinarily. It is intended for rheumatologists, general internists, specialists in related areas, and general practitioners in the country and abroad. It has become an important space in the work of all rheumatologists from Central and South America.

See more Open Access Option

Indexed in:

Scopus, SciELO, Latindex, Imbiomed, Lilacs, e-revist@s, Periódica and Embase.

Scleromyxoedema is a cutaneous fibromucinosis of unknown aetiology. It is associated with haematological dyscrasias and quite diverse manifestations. Pulmonary vascular involvement is rare and requires a differential diagnosis approach with systemic sclerosis. The case of a patient with scleromyxoedema with an extracutaneous pulmonary manifestation is described.

Keywords:

Scleromyxoedema

Pulmonary hypertension

Monoclonal gammopathy of undetermined significance

Resumen

El escleromixedema es una fibromucinosis cutánea de etiología desconocida. Se asocia a discrasias hematológicas y a manifestaciones sistémicas muy diversas. El compromiso vascular pulmonar es poco frecuente y requiere un abordaje de diagnóstico diferencial con la esclerosis sistémica. Se describe el caso de un paciente con escleromixedema con manifestación extracutánea pulmonar.

Palabras clave:

Escleromixedema

Hipertensión pulmonar

Gammapatía monoclonal de significado inciertoribed

Article

These are the options to access the full texts of the publication Revista Colombiana de Reumatología (English Edition)

Subscriber

If you already have your login data, please click here .

If you have forgotten your password you can you can recover it by clicking here and selecting the option “I have forgotten my password”

Purchase

Purchase article

Purchasing article the PDF version will be downloaded

Price 19.34 €

Purchase now

Contact

Phone for subscriptions and reporting of errors

From Monday to Friday from 9 a.m. to 6 p.m. (GMT + 1) except for the months of July and August which will be from 9 a.m. to 3 p.m.

Calls from Spain

932 415 960

Calls from outside Spain

+34 932 415 960

E-mail

atencionalcliente@elsevier.com

Publish in

Revista Colombiana de Reumatología

Tools

Indexed in:

Follow us:

Article

Subscribe to our newsletter