Article information
Resumen
Presentamos un artículo de revisión sobre las enfermedades autoinflamatorias, narrando su origen histórico y describiendo la estructura proteica y molecular del Inflamosoma, la clasificación actual de los trastornos autoinflamatorios y una descripción de las características inmunogenéticas y clínicas más sobresalientes de cada enfermedad.
Palabras clave:
enfermedades autoinflamatorias
inflamosoma
inflamosomopatías
criopirina.
Summary
We present a review article on the autoinflammatory diseases, narrating its historical origin and describing the protein and molecular structure of the Inflammasome, the current classification of the autoinflammatory diseases and a description of the immunogenetics and clinical characteristics more important of every disease.
Key words:
autoinflammatory diseases
inflammasome
inflammasomopathies
cryopyrin.
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