Image of the month
Oromandibular-limb hypogenesis syndromes (OLHS): A challenge for airway management
Síndromes de hipogenesia dactilooromandibular (OLHS): un reto para el manejo de la vía aérea
G. Villabona, I. Melgosa, F. Iglesias, A.M. González
Corresponding author
Sección de Anestesia Materno-Infantil, Servicio de Anestesiología y Reanimación, Hospital Universitario Marqués de Valdecilla, Santander, Spain
Read
1
Timeswas read the article
0
Total PDF
1
Total HTML
Share statistics
array:23 [ "pii" => "S2341192921001165" "issn" => "23411929" "doi" => "10.1016/j.redare.2020.07.010" "estado" => "S300" "fechaPublicacion" => "2021-10-01" "aid" => "1199" "copyright" => "Sociedad Española de Anestesiología, Reanimación y Terapéutica del Dolor" "copyrightAnyo" => "2020" "documento" => "article" "crossmark" => 1 "subdocumento" => "sco" "cita" => "Revista Española de Anestesiología y Reanimación (English Version). 2021;68:493-4" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:1 [ "total" => 0 ] "Traduccion" => array:1 [ "es" => array:19 [ "pii" => "S0034935620301912" "issn" => "00349356" "doi" => "10.1016/j.redar.2020.07.007" "estado" => "S300" "fechaPublicacion" => "2021-10-01" "aid" => "1199" "copyright" => "Sociedad Española de Anestesiología, Reanimación y Terapéutica del Dolor" "documento" => "article" "crossmark" => 1 "subdocumento" => "sco" "cita" => "Rev Esp Anestesiol Reanim. 2021;68:493-4" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:1 [ "total" => 0 ] "es" => array:11 [ "idiomaDefecto" => true "cabecera" => "<span class="elsevierStyleTextfn">IMAGEN DEL MES</span>" "titulo" => "Síndromes de hipogenesia dactilooromandibular (OLHS): un reto para el manejo de la vía aérea" "tienePdf" => "es" "tieneTextoCompleto" => "es" "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "493" "paginaFinal" => "494" ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "Oromandibular-limb hypogenesis syndromes (OLHS): a challenge for airway management" ] ] "contieneTextoCompleto" => array:1 [ "es" => true ] "contienePdf" => array:1 [ "es" => true ] "resumenGrafico" => array:2 [ "original" => 0 "multimedia" => array:7 [ "identificador" => "fig0005" "etiqueta" => "Figura 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 865 "Ancho" => 900 "Tamanyo" => 100353 ] ] "descripcion" => array:1 [ "es" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">Tomografía axial computarizada multicorte con reconstrucción 3D. Deformidad craneofacial, micrognatia, displasia-hipoplasia mandibular, disfunción de la articulación temporomandibular bilateral y deformidad dentoesquelética.</p>" ] ] ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "G. Villabona, I. Melgosa, F. Iglesias, A.M. González" "autores" => array:4 [ 0 => array:2 [ "nombre" => "G." "apellidos" => "Villabona" ] 1 => array:2 [ "nombre" => "I." "apellidos" => "Melgosa" ] 2 => array:2 [ "nombre" => "F." "apellidos" => "Iglesias" ] 3 => array:2 [ "nombre" => "A.M." "apellidos" => "González" ] ] ] ] ] "idiomaDefecto" => "es" "Traduccion" => array:1 [ "en" => array:9 [ "pii" => "S2341192921001165" "doi" => "10.1016/j.redare.2020.07.010" "estado" => "S300" "subdocumento" => "" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:1 [ "total" => 0 ] "idiomaDefecto" => "en" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S2341192921001165?idApp=UINPBA00004N" ] ] "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0034935620301912?idApp=UINPBA00004N" "url" => "/00349356/0000006800000008/v1_202109150618/S0034935620301912/v1_202109150618/es/main.assets" ] ] "itemAnterior" => array:19 [ "pii" => "S2341192921001219" "issn" => "23411929" "doi" => "10.1016/j.redare.2020.11.006" "estado" => "S300" "fechaPublicacion" => "2021-10-01" "aid" => "1261" "copyright" => "Sociedad Española de Anestesiología, Reanimación y Terapéutica del Dolor" "documento" => "simple-article" "crossmark" => 1 "subdocumento" => "cor" "cita" => "Revista Española de Anestesiología y Reanimación (English Version). 2021;68:491-2" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:1 [ "total" => 0 ] "en" => array:10 [ "idiomaDefecto" => true "cabecera" => "<span class="elsevierStyleTextfn">Letter to the Director</span>" "titulo" => "Use of clinical simulation to support a pediatric face mask procurement process" "tienePdf" => "en" "tieneTextoCompleto" => "en" "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "491" "paginaFinal" => "492" ] ] "titulosAlternativos" => array:1 [ "es" => array:1 [ "titulo" => "Empleo de la simulación clínica como apoyo al proceso de compra de mascarillas faciales pediátricas" ] ] "contieneTextoCompleto" => array:1 [ "en" => true ] "contienePdf" => array:1 [ "en" => true ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "C. Suarez, P. Hernández-Pinto, J. Manso, J.M. Maestre" "autores" => array:4 [ 0 => array:2 [ "nombre" => "C." "apellidos" => "Suarez" ] 1 => array:2 [ "nombre" => "P." "apellidos" => "Hernández-Pinto" ] 2 => array:2 [ "nombre" => "J." "apellidos" => "Manso" ] 3 => array:2 [ "nombre" => "J.M." "apellidos" => "Maestre" ] ] ] ] ] "idiomaDefecto" => "en" "Traduccion" => array:1 [ "es" => array:9 [ "pii" => "S0034935620303182" "doi" => "10.1016/j.redar.2020.11.006" "estado" => "S300" "subdocumento" => "" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:1 [ "total" => 0 ] "idiomaDefecto" => "es" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0034935620303182?idApp=UINPBA00004N" ] ] "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S2341192921001219?idApp=UINPBA00004N" "url" => "/23411929/0000006800000008/v1_202109260522/S2341192921001219/v1_202109260522/en/main.assets" ] "en" => array:13 [ "idiomaDefecto" => true "cabecera" => "<span class="elsevierStyleTextfn">Image of the month</span>" "titulo" => "Oromandibular-limb hypogenesis syndromes (OLHS): A challenge for airway management" "tieneTextoCompleto" => true "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "493" "paginaFinal" => "494" ] ] "autores" => array:1 [ 0 => array:4 [ "autoresLista" => "G. Villabona, I. Melgosa, F. Iglesias, A.M. González" "autores" => array:4 [ 0 => array:2 [ "nombre" => "G." "apellidos" => "Villabona" ] 1 => array:2 [ "nombre" => "I." "apellidos" => "Melgosa" ] 2 => array:2 [ "nombre" => "F." "apellidos" => "Iglesias" ] 3 => array:4 [ "nombre" => "A.M." "apellidos" => "González" "email" => array:1 [ 0 => "antoniomanuel.gonzalez@scsalud.es" ] "referencia" => array:1 [ 0 => array:2 [ "etiqueta" => "*" "identificador" => "cor0005" ] ] ] ] "afiliaciones" => array:1 [ 0 => array:2 [ "entidad" => "Sección de Anestesia Materno-Infantil, Servicio de Anestesiología y Reanimación, Hospital Universitario Marqués de Valdecilla, Santander, Spain" "identificador" => "aff0005" ] ] "correspondencia" => array:1 [ 0 => array:3 [ "identificador" => "cor0005" "etiqueta" => "⁎" "correspondencia" => "Corresponding author." ] ] ] ] "titulosAlternativos" => array:1 [ "es" => array:1 [ "titulo" => "Síndromes de hipogenesia dactilooromandibular (OLHS): un reto para el manejo de la vía aérea" ] ] "resumenGrafico" => array:2 [ "original" => 0 "multimedia" => array:8 [ "identificador" => "fig0015" "etiqueta" => "Figure 3" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr3.jpeg" "Alto" => 921 "Ancho" => 900 "Tamanyo" => 57557 ] ] "detalles" => array:1 [ 0 => array:3 [ "identificador" => "at0015" "detalle" => "Figure " "rol" => "short" ] ] "descripcion" => array:1 [ "en" => "<p id="spar0015" class="elsevierStyleSimplePara elsevierViewall">Multislice computed axial tomography. Dentoskeletal deformity and left septal deviation.</p>" ] ] ] "textoCompleto" => "<span class="elsevierStyleSections"><p id="par0005" class="elsevierStylePara elsevierViewall">Oromandibular-limb hypogenesis syndrome (Moebius syndrome; Hanhart syndrome, Charlie M syndrome; hypoglossia-hypodactyly syndrome) involves several congenital malformations, typically: microglossia, mandibular micrognathia and finger abnormalities. We present the case of a 7-year-old patient, weight 25 kg, diagnosed with Hanhart syndrome. He presented craniofacial deformity, micrognathia, mandibular hypoplasia (<a class="elsevierStyleCrossRef" href="#fig0005">Fig. 1</a>), retraction of the lower lip (<a class="elsevierStyleCrossRef" href="#fig0010">Fig. 2</a>), bifid uvula, undeveloped tongue, dentoskeletal deformity and left septal deviation (<a class="elsevierStyleCrossRef" href="#fig0015">Fig. 3</a>), adactylia of the second and third fingers on the right hand and the second, third and fourth fingers on the left hand, and limited oral opening (12 mm, forced to 22 mm). We performed 2 interventions with airway management using deep sedation under spontaneous ventilation using midazolam (0.05 mg/kg iv), atropine (0.01 mg/kg) and a propofol: ketamine combination (8:4 mg/ml) administered in a 0.25 ml/kg/2 min bolus and perfusion of 0.2 ml/kg/h. The first intervention was performed with videolaryngoscope-assisted right nasal intubation, and the second with right nasal fibreoptic bronchoscopy.</p><elsevierMultimedia ident="fig0005"></elsevierMultimedia><elsevierMultimedia ident="fig0010"></elsevierMultimedia><elsevierMultimedia ident="fig0015"></elsevierMultimedia></span>" "pdfFichero" => "main.pdf" "tienePdf" => true "NotaPie" => array:1 [ 0 => array:2 [ "etiqueta" => "☆" "nota" => "<p class="elsevierStyleNotepara" id="npar0005">Please cite this article as: Villabona G, Melgosa I, Iglesias F, González AM. Síndromes de hipogenesia dactilooromandibular (OLHS): un reto para el manejo de la vía aérea. Rev Esp Anestesiol Reanim. 2021;68:493–494.</p>" ] ] "multimedia" => array:3 [ 0 => array:8 [ "identificador" => "fig0005" "etiqueta" => "Figure 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 865 "Ancho" => 900 "Tamanyo" => 100353 ] ] "detalles" => array:1 [ 0 => array:3 [ "identificador" => "at0005" "detalle" => "Figure " "rol" => "short" ] ] "descripcion" => array:1 [ "en" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">Multislice computed axial tomography with 3D reconstruction. Craniofacial deformity, micrognathia, mandibular dysplasia-hypoplasia, bilateral temporomandibular joint dysfunction and dentoskeletal deformity.</p>" ] ] 1 => array:8 [ "identificador" => "fig0010" "etiqueta" => "Figure 2" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr2.jpeg" "Alto" => 1043 "Ancho" => 1000 "Tamanyo" => 124989 ] ] "detalles" => array:1 [ 0 => array:3 [ "identificador" => "at0010" "detalle" => "Figure " "rol" => "short" ] ] "descripcion" => array:1 [ "en" => "<p id="spar0010" class="elsevierStyleSimplePara elsevierViewall">Multislice computed axial tomography with 3D reconstruction. Lower lip retraction caused by the presence of scaring in the midline.</p>" ] ] 2 => array:8 [ "identificador" => "fig0015" "etiqueta" => "Figure 3" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr3.jpeg" "Alto" => 921 "Ancho" => 900 "Tamanyo" => 57557 ] ] "detalles" => array:1 [ 0 => array:3 [ "identificador" => "at0015" "detalle" => "Figure " "rol" => "short" ] ] "descripcion" => array:1 [ "en" => "<p id="spar0015" class="elsevierStyleSimplePara elsevierViewall">Multislice computed axial tomography. Dentoskeletal deformity and left septal deviation.</p>" ] ] ] ] "idiomaDefecto" => "en" "url" => "/23411929/0000006800000008/v1_202109260522/S2341192921001165/v1_202109260522/en/main.assets" "Apartado" => array:4 [ "identificador" => "70433" "tipo" => "SECCION" "en" => array:2 [ "titulo" => "Images of the month" "idiomaDefecto" => true ] "idiomaDefecto" => "en" ] "PDF" => "https://static.elsevier.es/multimedia/23411929/0000006800000008/v1_202109260522/S2341192921001165/v1_202109260522/en/main.pdf?idApp=UINPBA00004N&text.app=https://www.elsevier.es/" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S2341192921001165?idApp=UINPBA00004N" ]
| Year/Month | Html | Total | |
|---|---|---|---|
| 2023 March | 1 | 0 | 1 |
