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"apellidos" => "Perea Costa" "email" => array:1 [ 0 => "costa@ip.rm.cnr.rt" ] "referencia" => array:1 [ 0 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">*</span>" "identificador" => "cor0005" ] ] ] ] "afiliaciones" => array:1 [ 0 => array:1 [ "entidad" => "CNH-Istituto di Psicologia. Reparto di Neuropsicologia del Linguaggio e Sorditá. Roma. Italia." ] ] "correspondencia" => array:1 [ 0 => array:3 [ "identificador" => "cor0005" "etiqueta" => "*" "correspondencia" => "Correspondencia: CNH - Istituto di Psicologia Reparto di Neuropsicologia del Linguaggio e Sorditá Via Nomentana 56 00161 Roma (Italia)" ] ] ] ] "pdfFichero" => "main.pdf" "tienePdf" => true "PalabrasClave" => array:2 [ "es" => array:1 [ 0 => array:4 [ "clase" => "keyword" "titulo" => "Palabras clave" "identificador" => "xpalclavsec235102" "palabras" => array:7 [ 0 => "Sordera" 1 => "Ceguera" 2 => "Sordoceguera" 3 => "Retinitis Pigmentosa" 4 => "Ceguera nocturna" 5 => "Deslumbramientos" 6 => "Lengua de Signos" ] ] ] "en" => array:1 [ 0 => array:4 [ "clase" => "keyword" "titulo" => "Key words" "identificador" => "xpalclavsec235103" "palabras" => array:7 [ 0 => "Deafness" 1 => "Blindness" 2 => "Deafblindness" 3 => "Retinitis Pigmentosa" 4 => "Night blindness" 5 => "Glare" 6 => "Sign Language" ] ] ] ] "tieneResumen" => true "resumen" => array:2 [ "es" => array:2 [ "titulo" => "Resumen" "resumen" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">Este artículo pretende ofrecer información clara y concisa sobre el síndrome de Usher, tanto a padres afectados como a profesionales, con el objetivo de conseguir entre todos un diagnóstico precoz que minimice los efectos del síndrome –a través de una intervención educativa temprana y eficaz– y garantice una mayor calidad de vida a todos los afectados desde la misma infancia. Puntos clave del artículo: definición, tipología, signos que pueden alertar a la familia o al personal escolar sobre la presencia de retinitis pigmentosa, implicaciones psico-educativas y asociaciones/organizaciones nacionales e internacionales relacionadas con el síndrome de Usher.</p>" ] "en" => array:2 [ "titulo" => "Summary" "resumen" => "<p id="spar0010" class="elsevierStyleSimplePara elsevierViewall">This article intend to provide brief and clear information on the Usher Syndrome specially addressed to people with Usher Syndrome, to their relatives and to professionals working in the fields of deafness, blindness and deafblindness. The aim is to get an early detection of the Syndrome which minimize its effects and ensure a greater quality of life to every affected person from his/her earlier childhood. 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El síndrome de usher: importancia de un diagnóstico precoz. implicaciones educativas
M.L. Perea Costa
Autor para correspondencia
costa@ip.rm.cnr.rt
Correspondencia: CNH - Istituto di Psicologia Reparto di Neuropsicologia del Linguaggio e Sorditá Via Nomentana 56 00161 Roma (Italia)
Correspondencia: CNH - Istituto di Psicologia Reparto di Neuropsicologia del Linguaggio e Sorditá Via Nomentana 56 00161 Roma (Italia)
CNH-Istituto di Psicologia. Reparto di Neuropsicologia del Linguaggio e Sorditá. Roma. Italia.